The pulmonary arteries arise from the 6th aortic arch. The involution of the ipsilateral proximal 6th aortic arch may result in unilateral absent pulmonary artery (UAPA). Unilateral absent pulmonary artery is a rare disorder with an estimated prevalence of 1 in 200,000 adults.We report a case of absent right pulmonary artery with bronchiectasis presenting as obstructive airway disease (OAD).A 40yearold female presented with acute onset of fever, shortness of breath, cough and mucoid sputum production for 4 days. She had a past history of OAD since 15years.On investigation, Chest X ray showed trachea shifted to right, smaller right lung with a small hilar shadow on right side. CECT Thorax showed right side bronchiectasis with small right lung with absent right pulmonary artery, cardiomegaly & Pulmonary hypertension. Patient was treated with IV antibiotics, bronchodilators, mucolytics, moist O2, antihypertensive. Patient clinically improved and was discharged as obstructive airway disease